About Ehler’s Danlos Syndrome
Ehler’s Danlos Sydnrome [EDS] is an inherited, genetic condition affecting collagen in the body’s tissues. There are 6 subtypes of EDS with different clinical presentations, however; patients can exhibit symptoms which cross over between types.
There are common symptoms between most sub-types, and the skin is one of the most commonly involved tissues. EDS was first described thousands of years ago—albeit briefly— but it wasn’t until the 1800’s that Tschernogobow made the first clinical description of the condition. Later, the condition would be named after Danish dermatologist Edward Ehlers and French doctor Henri-Alexandre Danlos.
The six types of EDS include:
The most common complaints across all types are increased skin elasticity, thinner skin, easy bruising and scarring. The severity of the conditions varies between individuals, but not within families. That is to say those children of parents with moderate classic EDS are likely to present in with similar disease severity.
People with EDS often have skin that is described as velvety, and it may be a lot stretchier than other skin. The skin may also be thinner, having an almost translucent property where the vessels are easily seen. Over time, the changes in collagen may lead to early wrinkling. Therefore it is important for people with EDS to prevent sun damage by using adequate sun protection including a high SPF sunscreen, large hats, long clothing and sunglasses.
Easy bruising is really annoying for people with EDS who might sustain large, deep bruises after even the smallest bumps. The small blood vessels have a tougher time of healing quickly than normal. Using ice packs on bumps and applying bruise healing medicines can help reduce the appearance of large bruises.
The skin is more likely to scar with appearance known as cigarette paper scarring. There may also be delayed wound healing (which is a double whammy for scarring risk) prior to the formation of the scar. All patients are encouraged to use scar massage and topical gels to reduce scar tissue. Vitamin C has also been identified as a potential treatment during wound and scar healing periods, as it used in the synthesis of collagen; research continues in this area.
If you require personalised skincare based for your specific skin type contact your local doctor, who will arrange for you to see a Dermatologist. We‘ll provide you with a straightforward, efficient and very effective treatment plan targeted to your concerns. Contact us today.